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Article

Desmoplakin Cardiomyopathy.

The international journal of cardiovascular imaging - 1 Aug 2026

Han Daniel D, Jew Gregory, Kaproth-Joslin Katherine

Abstract excerpt

Desmoplakin (DSP) cardiomyopathy is an inherited condition caused by desmosome gene DSP mutation, resulting in arrhythmias, heart failure, and sudden cardiac death. Cardiac MRI typically presents with ring-like subepicardial late gadolinium enhancement which can be mistaken for myocarditis or fatty replacement.

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Methodology Data sources Editorial policy Privacy Delete account & data About Contact Helena Bioinformatics

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Source

Identifiers

PMID: 41796267
DOI: 10.1007/s10554-026-03670-4

Genes

DSP

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 21 Oct 2026.

Related research

Semantic proximity does not establish scientific evidence. Graph snapshot: 2026-09-29.

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