Article
Predictors of proteinuria, amyloidosis and kidney failure in familial Mediterranean fever: data from the International AIDA Network Registry.
Rheumatology (Oxford, England) - 1 Aug 2025
Vitale Antonio, Caggiano Valeria, Sbalchiero Jessica, Tufan Abdurrahman, Batu Ezgi Deniz, Ragab Gaafar, Portincasa Piero, Conti Giovanni, Aragona Emma, Sota Jurgen, Gavioli Francesco, Gaggiano Carla, De Paulis Amato, Şahin Ali, Maggio Maria Cristina, Rigante Donato, Olivieri Alma Nunzia, Yildirim Derya, Kucuk Hamit, Kardas Riza Can, Vasi Ibrahim, Ozen Seza, Bilginer Yelda, Sener Seher, Emreol Hulya Ercan, Mahmoud Ayman Abdel-Monem Ahmed, Ghanema Mahmoud, Maher Amina, Saad Moustafa Ali, Jaber Nour, Khalil Mohamad, Di Ciaula Agostino, De Palma Ludovica, Cuzzola Renata, Affronti Andrea, Gambino Fabrizio, Della Casa Francesca, Mormile Ilaria, Babayiğit Arif, Çelik Neşe Çabuk, Gicchino Maria Francesca, Jahnz-Rozyk Karina, La Torre Francesco, Insalaco Antonella, Recke Andreas, Del Giudice Emanuela, Barone Patrizia, Cattalini Marco, Brucato Antonio Luca, Opris-Belinski Daniela, Sfikakis Petros P, Li Gobbi Francesca, Emmi Giacomo, Giardini Henrique A Mayrink, Hernández-Rodríguez José, Parronchi Paola, Ruscitti Piero, Costi Stefania, Tharwat Samar, Karamanakos Anastasios, Sfriso Paolo, Conforti Alessandro, Verrecchia Elena, Lopalco Giuseppe, Ogunjimi Benson, Wiesik-Szewczyk Ewa, Balistreri Alberto, Fabiani Claudia, Frediani Bruno, Cantarini Luca
Abstract excerpt
OBJECTIVES: Proteinuria, amyloidosis and kidney failure are the main long-term renal complications of FMF. This study assesses their risk factors, independent of ethnicity or residence. METHODS: Patients' data were drawn from the International AIDA Network registry for monogenic autoinflammatory diseases. RESULTS: A total of 598 FMF patients were enrolled, with 80 having proteinuria, 61 amyloidosis and 25 kidney...
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