Article
Elexacaftor/Tezacaftor/Ivacaftor Improves Bronchial Artery Dilatation Detected by Magnetic Resonance Imaging in Patients with Cystic Fibrosis.
Annals of the American Thoracic Society - 1 Nov 2023
Wucherpfennig Lena, Triphan Simon M F, Wege Sabine, Kauczor Hans-Ulrich, Heussel Claus P, Sommerburg Olaf, Stahl Mirjam, Mall Marcus A, Eichinger Monika, Wielpütz Mark O
Abstract excerpt
Rationale: Magnetic resonance imaging (MRI) detects improvements in mucus plugging and bronchial wall thickening, but not in lung perfusion in patients with cystic fibrosis (CF) treated with elexacaftor/tezacaftor/ivacaftor (ETI). Objectives: To determine whether bronchial artery dilatation (BAD), a key feature of advanced lung disease, indicates irreversibility of perfusion abnormalities and whether BAD could be...
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