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Article

[Cystic fibrosis with focal biliary cirrhosis and portal hypertension in Japan: a case report].

Nihon Shokakibyo Gakkai zasshi = The Japanese journal of gastro-enterology - 1 Jan 2021

Yamamoto Akiko, Ito Koichi, Naruse Satoru, Hattori Hideo, Nakakuki Miyuki, Fujiki Kotoyo, Ishiguro Hiroshi

Abstract excerpt

A 9-year-old Japanese girl was found to have persistently elevated hepatic enzymes, chronic bronchitis, chronic sinusitis, and poor weight gain beginning at 5 months of age. Chest computed tomography (CT) revealed diffuse bronchial wall thickening and peripheral bronchiectasis. Abdominal CT showed pancreatic atrophy, liver cirrhosis, a dilated splenic vein, and splenomegaly. Her sweat chloride concentration was...

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Source

Identifiers

PMID: 34248082
DOI: 10.11405/nisshoshi.118.686

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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