Article
Sarcoidosis and IPF in the same patient-a coincidence, an association or a phenotype?
Respiratory medicine - 1 Nov 2018
Collins Bridget F, McClelland Robyn L, Ho Lawrence A, Mikacenic Carmen R, Hayes Jennifer, Spada Carolyn, Raghu Ganesh
Abstract excerpt
BACKGROUND: Idiopathic Pulmonary Fibrosis (IPF) and Sarcoidosis are distinct clinical entities. Fibrotic disease in pulmonary sarcoidosis is typically upper lobe predominant. In IPF fibrosis is basilar and peripheral predominant [usual interstitial pneumonia (UIP) pattern]. Sarcoidosis and UIP have rarely been observed in the same patient. We sought to characterize patients manifesting both sarcoidosis and IPF...
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