Article
Long-term survival and phenotypic spectrum in heterotaxy syndrome: A 25-year follow-up experience.
International journal of cardiology - 1 Oct 2018
Baban Anwar, Cantarutti Nicoletta, Adorisio Rachele, Lombardi Roberta, Calcagni Giulio, Piano Mortari Eva, Dallapiccola Bruno, Marino Bruno, Iorio Fiore Salvatore, Carsetti Rita, Digilio Maria Cristina, Giannico Salvatore, Drago Fabrizio, Carotti Adriano
Abstract excerpt
BACKGROUND: Heterotaxy syndrome (HS) is a group of congenital disorders characterized by abnormal arrangement of thoraco-abdominal organs across the left-right axis of the body, classified as right (RAI) and left atrial isomerism (LAI)·We investigated the long-term survival and phenotypic spectrum in our HS cohort. Results are compared to literature data. METHODS: This is a single centre, observational, both...
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