Article
Gastrointestinal pathophysiology and nutrition in cystic fibrosis.
Expert review of gastroenterology & hepatology - 1 Sept 2018
Ratchford Thomas L, Teckman Jeffrey H, Patel Dhiren R
Abstract excerpt
INTRODUCTION: Cystic fibrosis (CF) is a severe, progressive, multisystemic disease that is caused by mutations in the cystic fibrosis transmembrane conductance regulator gene. Optimizing nutrition is critical, as higher growth parameters are associated with better pulmonary function and outcomes, but unfortunately patients with this disease are prone to malnutrition, growth failure, and vitamin deficiencies. The...
Topics
- Adolescent
- Adolescent Development
- Adolescent Nutritional Physiological Phenomena
- Child
- Child Development
- Child Nutritional Physiological Phenomena
- Child, Preschool
- Cystic Fibrosis
- Cystic Fibrosis Transmembrane Conductance Regulator
- Gastrointestinal Diseases
- Gastrointestinal Tract
- Humans
- Infant
- Infant Nutritional Physiological Phenomena
- Infant, Newborn
- Malnutrition
- Mutation
- Nutritional Status
