Disappearance of recurrent pancreatitis after splenectomy in familial chylomicronemia syndrome.

Abstract excerpt

BACKGROUND AND AIMS: Recurrent pancreatitis is a severe complication of familial chylomicronemia syndrome (FCS) mainly secondary to lipoprotein lipase deficiency. The mechanism and interindividual variability of pancreatitis in FCS are not fully understood, but abnormalities in the drainage system of pancreatic veins could be involved. METHODS AND RESULTS: Two cases of typical FCS are described with a past...

Topics

Share this publication in a Topic to start or enrich a Post.

• Share to Aged
• Share to Genetic Predisposition to Disease
• Share to Hyperlipoproteinemia Type I