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Article

Automated segmentation reveals silent radiographic progression in adult-onset vanishing white-matter disease.

The neuroradiology journal - 1 Feb 2017

Huber Thomas, Herwerth Marina, Alberts Esther, Kirschke Jan S, Zimmer Claus, Ilg Ruediger

Abstract excerpt

Adult-onset vanishing white-matter disease (VWM) is a rare autosomal recessive disease with neurological symptoms such as ataxia and paraparesis, showing extensive white-matter hyperintensities (WMH) on magnetic resonance (MR) imaging. Besides symptom-specific scores like the International Cooperative Ataxia Rating Scale (ICARS), there is no established tool to monitor disease progression. Because of extensive...

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PMID: 27864579
DOI: 10.1177/1971400916678222
PMCID: PMC5564332

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026. Manifest publication-graph-cohort-2026-09-06.1.

Source receipt: pubmed, retrieved 6 Sept 2026.

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