Article
Malignant pheochromocytoma in a 16-year-old patient with neurofibromatosis type 1.
Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology Society - 1 Jan 2000
Giovannoni Isabella, Callea Francesco, Boldrini Renata, Inserra Alessandro, Cozza Raffaele, Francalanci Paola
Abstract excerpt
Patients with neurofibromatosis type I (NF1) feature a high risk of developing benign and malignant tumors, mainly those with a neuroectodermal origin, the risk being about 4 times higher than in the general population. Pheochromocytoma (PHEO) is a sporadic tumor (1∶100,000) arising from the adrenal medulla. Pheochromocytoma is a rare condition when occurring in conjunction with NF1 and occurs in about 1% of...
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