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Article

The effect of valinomycin in fibroblasts from patients with fatty acid oxidation disorders.

Biochemical and biophysical research communications - 9 Aug 2013

Ndukwe Erlingsson Uzochi Chimdinma, Iacobazzi Francesco, Liu Aiping, Ardon Orly, Pasquali Marzia, Longo Nicola

Abstract excerpt

Disorders of the carnitine cycle and of the beta oxidation spiral impair the ability to obtain energy from fats at time of fasting and stress. This can result in hypoketotic hypoglycemia, cardiomyopathy, cardiac arrhythmia and other chronic medical problems. The in vitro study of fibroblasts from patients with these conditions is impaired by their limited oxidative capacity. Here we evaluate the capacity of...

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Identifiers

PMID: 23867825
DOI: 10.1016/j.bbrc.2013.07.020
PMCID: PMC3773513

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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