Article
Clinical features and course of refractory anemia with ring sideroblasts associated with marked thrombocytosis.
Haematologica - 1 Jul 2012
Broseus Julien, Florensa Lourdes, Zipperer Esther, Schnittger Susanne, Malcovati Luca, Richebourg Steven, Lippert Eric, Cermak Jaroslav, Evans Jyoti, Mounier Morgane, Raya José Maria, Bailly François, Gattermann Norbert, Haferlach Torsten, Garand Richard, Allou Kaoutar, Besses Carlos, Germing Ulrich, Haferlach Claudia, Travaglino Erica, Luno Elisa, Pinan Maria Angeles, Arenillas Leonor, Rozman Maria, Perez Sirvent Maria Luz, Favre Bernardine, Guy Julien, Alonso Esther, Ahwij Nuhri, Jerez Andrés, Hermouet Sylvie, Maynadié Marc, Cazzola Mario, Girodon François
Abstract excerpt
BACKGROUND: Refractory anemia with ring sideroblasts associated with marked thrombocytosis was proposed as a provisional entity in the 2001 World Health Organization classification of myeloid neoplasms and also in the 2008 version, but its existence as a single entity is contested. We wish to define the clinical features of this rare myelodysplastic/myeloproliferative neoplasm and to compare its clinical outcome...
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