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Article

The Schnitzler syndrome.

Orphanet journal of rare diseases - 8 Dec 2010

Lipsker Dan

Abstract excerpt

The Schnitzler syndrome is a rare and underdiagnosed entity which is considered today as being a paradigm of an acquired/late onset auto-inflammatory disease. It associates a chronic urticarial skin rash, corresponding from the clinico-pathological viewpoint to a neutrophilic urticarial dermatosis, a monoclonal IgM component and at least 2 of the following signs: fever, joint and/or bone pain, enlarged lymph...

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Source

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Identifiers

PMID: 21143856
DOI: 10.1186/1750-1172-5-38
PMCID: PMC3018454

Genes

NLRP3

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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