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Article

Long QT syndrome due to a novel mutation in SCN5A: treatment with ICD placement at 1 month and left cardiac sympathetic denervation at 3 months of age.

Journal of interventional cardiac electrophysiology : an international journal of arrhythmias and pacing - 1 Oct 2009

Silver Eric S, Liberman Leonardo, Chung Wendy K, Spotnitz Henry M, Chen Jonathan M, Ackerman Michael J, Moir Christopher, Hordof Allan J, Pass Robert H

Abstract excerpt

We describe the case of a newborn with congenital long QT syndrome, with 2:1 AV block and frequent episodes of Torsades de Pointes (TdP) requiring placement of a dual chamber ICD at 33 days and 3.63 kg, the youngest and smallest patient, thus far reported. Long QT syndrome was diagnosed due to bradycardia in the newborn nursery, with frequent episodes of TdP. The patient was initially treated with magnesium and...

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Identifiers

PMID: 19669871
DOI: 10.1007/s10840-009-9428-1
PMCID: PMC3332535

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