Article
Fever of unclear origin and cytopenia because of acute splenic sequestration in a young immunocompetent carrier of beta-globin mutation for Hb Valletta.
The American journal of the medical sciences - 1 Dec 2008
Parrinello Gaspare, Torres Daniele, Paterna Salvatore, Di Pasquale Pietro, Licata Giuseppe
Abstract excerpt
Fever of unclear origin is a clinical challenge in medical practice. Infectious diseases, neoplasms, and collagen vascular illnesses are its main causes in adults and children. Acute splenic sequestration crises, a known potentially fatal complication of sickle cell disease and sickle beta-thalassemia, are uncommon in beta-heterozygosis. We describe a case of prolonged recurrent episodes of fever with spontaneous...
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