Article
A scoring system for the classification of beta-thalassemia/Hb E disease severity.
American journal of hematology - 1 Jun 2008
Sripichai Orapan, Makarasara Wattanan, Munkongdee Thongperm, Kumkhaek Chutima, Nuchprayoon Issarang, Chuansumrit Ampaiwan, Chuncharunee Suporn, Chantrakoon Nawarat, Boonmongkol Piathip, Winichagoon Pranee, Fucharoen Suthat
Abstract excerpt
Beta-thalassemia intermediate patients show a remarkable clinical heterogeneity. We examined the phenotypic diversity of 950 beta-thalassemia/Hb E patients in an attempt to construct a system for classifying disease severity. A novel scoring system based on six independent parameters, hemoglobin level, age at disease presentation, age at receiving first blood transfusion, requirement for transfusion, spleen size,...
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