Article
Severe, obstructive biventricular hypertrophy in a patient with Costello syndrome: Clinical impact and management.
International journal of cardiology - 28 Nov 2008
Limongelli Giuseppe, Pacileo Giuseppe, Digilio Maria Cristina, Calabro' Paolo, Di Salvo Giovanni, Rea Alessandra, Miele Tiziana, Frigiola Alessandro, Sarkozy Anna, Dallapiccola Bruno, Marino Bruno, Calabro' Raffaele
Abstract excerpt
We report a severe, biventricular obstructive cardiomyopathy in a young female with Costello syndrome, who underwent a right ventricular myectomy for symptoms relief. We discuss potential clinical implications and management of severe hypertrophy in Costello syndrome.
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