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Article

Pleuropulmonary pathology of Birt-Hogg-Dubé syndrome.

The American journal of surgical pathology - 1 Mar 2006

Butnor Kelly J, Guinee Donald G

Abstract excerpt

Birt-Hogg-Dubé (BHD) syndrome is a rare inherited genodermatosis characterized by distinctive cutaneous lesions, an increased risk of renal and colonic neoplasia, and the development of pleuropulmonary blebs and cysts. Although the pathology of renal and cutaneous manifestations of BHD has been well described, few reports have detailed the pathologic features of pulmonary involvement. Herein we present the...

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Identifiers

PMID: 16538061
DOI: 10.1097/01.pas.0000183571.17011.06

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

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