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Article

Mammalian N-acetylglutamate synthase.

Molecular genetics and metabolism - 1 Apr 2004

Morizono Hiroki, Caldovic Ljubica, Shi Dashuang, Tuchman Mendel

Abstract excerpt

N-Acetylglutamate synthase (NAGS, E.C. 2.3.1.1) is a mitochondrial enzyme that catalyzes the formation of N-acetylglutamate (NAG), an essential allosteric activator of carbamylphosphate synthetase I (CPSI). The mouse and human NAGS genes have been identified based on similarity to regions of NAGS from Neurospora crassa and cloned from liver cDNA libraries. These genes were shown to complement an argA- (NAGS)...

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Source

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Identifiers

PMID: 15050968
DOI: 10.1016/j.ymgme.2003.10.017
PMCID: PMC3031861

Genes

NAGS

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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