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Article

Molecular pathways of oligodendrocyte apoptosis revealed by mutations in the proteolipid protein gene.

Microscopy research and technique - 15 Mar 2001

Southwood C, Gow A

Abstract excerpt

A decade after the genetic link was established between mutations in the proteolipid protein gene and two leukodystrophies, Pelizaeus-Merzbacher disease and spastic paraplegia, the molecular mechanisms underlying pathogenesis are beginning to come to light. Data from animal models of these diseas...

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Identifiers

PMID: 11276122
DOI: 10.1002/jemt.1054

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 2 Sept 2026. Prepared record publication-11276122-2026-09-02.2. Manifest publication-graph-cohort-2026-09-02.2.

Source receipt: PubMed via Helena Literature Corpus, retrieved 2 Sept 2026.

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Molecular pathways of oligodendrocyte apoptosis revealed by mutations in the proteolipid protein gene.PMID 11276122Read ↗

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