Article
Phenotypic patterns and outcomes of connective tissue disease-associated pulmonary arterial hypertension: a Saudi single center experience.
Respiratory medicine - 1 Sept 2026
Alturaif Noura, Alhammad Saleh, Desai Sameer, Alahmadi Fayez, Alharbi Nadeen, Zaytoun Hamdeia, Alhamoud Hanadi, Alzubi Fatima, Aldalaan Abdullah M, Alduraibi Fatima K
Abstract excerpt
BACKGROUND: CTD-PAH is a heterogeneous condition with poor prognosis. While systemic sclerosis predominates in Western cohorts, systemic lupus erythematosus is a major contributor in Saudi Arabia and other non-Western regions. However, data on phenotypes, outcomes, and longitudinal risk stratification in Middle Eastern CTD-PAH remain limited. This study characterized CTD-PAH in a Saudi cohort and identified...
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