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Article

Natural History of Sensorineural Hearing Loss in Children With STRC Mutations.

The Laryngoscope - 1 Jun 2026

Chan Kenny H, Nightengale Emily E, Ekhteraei Setareh, Schicke Ericka, Tong Suhong, Zhu Austin, Burton Barbara K

Abstract excerpt

INTRODUCTION: The most common genes responsible for autosomal recessive nonsyndromic hearing loss (AR-NSHL) are GJB2 and STRC. STRC mutations are associated with mild-to-moderate sensorineural (SNHL) hearing loss and a lack of progression. However, our institutional experience suggested otherwise, prompting this review. METHODS: A 10-year retrospective chart review was performed at a tertiary children's hospital...

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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

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Source

Identifiers

PMID: 41623227
DOI: 10.1002/lary.70404

Genes

STRC
GJB2
AR
CATSPER2

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026.

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