Article
A pediatric cystic fibrosis arthropathy case who responded to Elexacaftor/Tezacaftor/Ivacaftor therapy.
Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society - 1 Nov 2023
Arslan Meliksah, Bahadir Zeynep, Basiaga Matthew L, Chalmers Sarah J, Demirel Nadir
Abstract excerpt
Cystic fibrosis arthropathy (CFA) is a transient, intermittent form of arthritis that cannot be associated with any other disease other than CF thus making CFA a diagnosis of exclusion. NSAIDs, short-term intermittent splinting, glucocorticoids, and disease-modifying anti-rheumatic drugs are treatment options for CFA. Currently, there is no consensus on how to best treat CFA. Diagnosis and treatment of CFA remain...
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