Article
Management of acute sloughing of the esophageal lining in patients with dystrophic epidermolysis bullosa-A series of six pediatric patients.
Pediatric dermatology - 1 Jan 2000
Bageta Maria Laura, Yerlett Natalie, Rybak Anna, Balboa Pablo Lopez, Petrof Gabriela, Martinez Anna E
Abstract excerpt
BACKGROUND: Dystrophic epidermolysis bullosa (DEB) is a subtype of an inherited skin disorder characterized by skin and mucosal fragility due to collagen VII (COL7A1) gene mutations. Esophageal strictures leading to chronic dysphagia and acute episodes are well recognized complications within this subtype. Sloughing of esophageal mucosa and the treatment of this emergency have heretofore received limited...
Read the complete abstract on PubMedTopics
Share this publication in a Topic to start or enrich a Post.
