Article
Brazilian guidelines for the pharmacological treatment of the pulmonary symptoms of cystic fibrosis. Official document of the Sociedade Brasileira de Pneumologia e Tisiologia (SBPT, Brazilian Thoracic Association).
Jornal brasileiro de pneumologia : publicacao oficial da Sociedade Brasileira de Pneumologia e Tisilogia - 1 Jan 2023
Athanazio Rodrigo Abensur, Tanni Suzana Erico, Ferreira Juliana, Dalcin Paulo de Tarso Roth, Fuccio Marcelo B de, Esposito Concetta, Canan Mariane Gonçalves Martynychen, Coelho Liana Sousa, Firmida Mônica de Cássia, Almeida Marina Buarque de, Marostica Paulo José Cauduro, Monte Luciana de Freitas Velloso, Souza Edna Lúcia, Pinto Leonardo Araujo, Rached Samia Zahi, Oliveira Verônica Stasiak Bednarczuk de, Riedi Carlos Antonio, Silva Filho Luiz Vicente Ribeiro Ferreira da
Abstract excerpt
Cystic fibrosis (CF) is a genetic disease that results in dysfunction of the CF transmembrane conductance regulator (CFTR) protein, which is a chloride and bicarbonate channel expressed in the apical portion of epithelial cells of various organs. Dysfunction of that protein results in diverse clinical manifestations, primarily involving the respiratory and gastrointestinal systems, impairing quality of life and...
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