Article
Biphenotypic Sinonasal Sarcoma: Case Reports of Diagnostic Findings and Clinical Management of 3 Cases.
Anticancer research - 1 Apr 2023
Augustin Yolanda, Zaidi Shane, Jones Robin L, Benson Charlotte, Simcock Richard, Fisher Cyril, Thway Khin, Hallin Magnus, Miah Aisha B
Abstract excerpt
BACKGROUND: Biphenotypic sinonasal sarcoma (BSNS) is a rare spindle cell sarcoma distinctly arising in the sinonasal area, with dual myogenic and neural differentiation, and characterised by the presence of PAX3 gene fusion, typically with MAML3. Although the majority may be indolent, up to 25% of cases reported in the literature are locally aggressive, with invasion of adjacent critical structures in the head...
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