Article
Geographical heterogeneity of clinical and serological phenotypes of systemic sclerosis observed at tertiary referral centres. The experience of the Italian SIR-SPRING registry and review of the world literature.
Autoimmunity reviews - 1 Oct 2022
Ferri Clodoveo, De Angelis Rossella, Giuggioli Dilia, Bajocchi Gianluigi, Dagna Lorenzo, Zanframundo Giovanni, Foti Rosario, Cacciapaglia Fabio, Cuomo Giovanna, Ariani Alarico, Rosato Edoardo, Guiducci Serena, Girelli Francesco, Riccieri Valeria, Zanatta Elisabetta, Bosello Silvia, Cavazzana Ilaria, Ingegnoli Francesca, De Santis Maria, Murdaca Giuseppe, Abignano Giuseppina, Romeo Nicoletta, Della Rossa Alessandra, Caminiti Maurizio, Iuliano Annamaria, Ciano Giovanni, Beretta Lorenzo, Bagnato Gianluca, Lubrano Ennio, De Andres Ilenia, Giollo Alessandro, Saracco Marta, Agnes Cecilia, Lumetti Federica, Spinella Amelia, Magnani Luca, Campochiaro Corrado, De Luca Giacomo, Codullo Veronica, Visalli Elisa, Masini Francesco, Gigante Antonietta, Bellando-Randone Silvia, Pellegrino Greta, Pigatto Erika, Lazzaroni Maria Grazia, Franceschini Franco, Generali Elena, Mennillo Gianna, Barsotti Simone, Mariano Giuseppa Pagano, Calabrese Francesca, Furini Federica, Vultaggio Licia, Parisi Simone, Peroni Clara Lisa, Rozza Davide, Zanetti Anna, Carrara Greta, Landolfi Giampiero, Scirè Carlo Alberto, Bianchi Gerolamo, Fusaro Enrico, Sebastiani Gian Domenico, Govoni Marcello, D'Angelo Salvatore, Cozzi Franco, Doria Andrea, Iannone Florenzo, Salvarani Carlo, Matucci-Cerinic Marco
Abstract excerpt
INTRODUCTION: Systemic sclerosis (SSc) is characterized by a complex etiopathogenesis encompassing both host genetic and environmental -infectious/toxic- factors responsible for altered fibrogenesis and diffuse microangiopathy. A wide spectrum of clinical phenotypes may be observed in patients' populations from different geographical areas. We investigated the prevalence of specific clinical and serological...
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