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Article

Ulnar Artery Aneurysm as a Late Sequela of Marfan Syndrome.

The Journal of hand surgery - 1 Nov 2020

Goodenough Christopher J, Afifi Rana O, Prakash Siddharth K, Buja L Maximilian, Lamaris Grigorios A

Abstract excerpt

Marfan syndrome (MFS) is a connective tissue disorder caused by mutations of the FBN1 gene encoding fibrillin-1, which leads to overexpression of transforming growth factor-β, increased hyaluronan deposition, and matrix metalloproteinase activity in the media of the aorta and other muscular arteries. Marfan syndrome patients present with connective tissue laxity and aneurysmal changes to muscular arteries....

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Identifiers

PMID: 32213296
DOI: 10.1016/j.jhsa.2020.01.010

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026. Manifest publication-graph-cohort-2026-09-06.1.

Source receipt: pubmed, retrieved 6 Sept 2026.

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