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Article

Extracellular matrix-driven congenital muscular dystrophies.

Matrix biology : journal of the International Society for Matrix Biology - 1 Oct 2018

Mohassel Payam, Foley A Reghan, Bönnemann Carsten G

Abstract excerpt

Skeletal muscle function relies on the myofibrillar apparatus inside myofibers as well as an intact extracellular matrix surrounding each myofiber. Muscle extracellular matrix (ECM) plays several roles including but not limited to force transmission, regulation of growth factors and inflammatory responses, and influencing muscle stem cell (i.e. satellite cell) proliferation and differentiation. In most...

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Identifiers

PMID: 29933045
DOI: 10.1016/j.matbio.2018.06.005

Genes

LAMA2

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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