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Article

Infants with Atypical Presentations of Alveolar Capillary Dysplasia with Misalignment of the Pulmonary Veins Who Underwent Bilateral Lung Transplantation.

The Journal of pediatrics - 1 Mar 2018

Towe Christopher T, White Frances V, Grady R Mark, Sweet Stuart C, Eghtesady Pirooz, Wegner Daniel J, Sen Partha, Szafranski Przemyslaw, Stankiewicz Pawel, Hamvas Aaron, Cole F Sessions, Wambach Jennifer A

Abstract excerpt

OBJECTIVE: To describe disease course, histopathology, and outcomes for infants with atypical presentations of alveolar capillary dysplasia with misalignment of the pulmonary veins (ACDMPV) who underwent bilateral lung transplantation. STUDY DESIGN: We reviewed clinical history, diagnostic studies, explant histology, genetic sequence results, and post-transplant course for 6 infants with atypical ACDMPV who...

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Methodology Data sources Editorial policy Privacy Delete account & data About Contact Helena Bioinformatics

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Identifiers

PMID: 29198536
DOI: 10.1016/j.jpeds.2017.10.026
PMCID: PMC5826830

Genes

FOXF1

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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