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Article

Lhermitte-Duclos disease with neurofibrillary tangles in heterotopic cerebral grey matter.

Folia neuropathologica - 1 Jan 2016

Rusiecki D, Lach B

Abstract excerpt

Lhermitte-Duclos disease (LDD), a disorder first described by French physicians Lhermitte and Duclos in 1920 [25], is a benign, slow growing dysplastic gangliocytoma of the cerebellum, characterized by replacement of the granule cell layer by abnormal granule and Purkinje like cells. The most frequent presenting signs and symptoms are megalocephaly, increased intracranial pressure, nausea, hydrocephalus, ataxia,...

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Source

Identifiers

PMID: 27543776
DOI: 10.5114/fn.2016.60434

Genes

PTEN

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 5 Sept 2026. Manifest publication-graph-cohort-2026-09-05.1.

Source receipt: pubmed, retrieved 5 Sept 2026.

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