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Article

CT-defined phenotype of pulmonary artery stenoses in Alagille syndrome.

Pediatric radiology - 1 Jul 2016

Rodriguez Renee M, Feinstein Jeffrey A, Chan Frandics P

Abstract excerpt

BACKGROUND: Alagille syndrome is a rare disorder commonly associated with pulmonary artery stenosis. Studies exist discussing the cardiovascular sequela but no consistent phenotype, or pattern of pulmonary artery stenosis, has been described. OBJECTIVE: The objective of this study was to characterize the distribution and severity of pulmonary artery stenosis in patients with Alagille syndrome based on computed...

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Identifiers

PMID: 27041277
DOI: 10.1007/s00247-016-3580-4

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LPA

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026. Manifest publication-graph-cohort-2026-09-06.1.

Source receipt: pubmed, retrieved 6 Sept 2026.

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