Article
The protean ocular involvement in monogenic autoinflammatory diseases: state of the art.
Clinical rheumatology - 1 Jul 2015
Bascherini Vittoria, Granato Carmela, Lopalco Giuseppe, Emmi Giacomo, Vannozzi Lorenzo, Bacherini Daniela, Franceschini Rossella, Iannone Florenzo, Salerni Annabella, Molinaro Francesco, Messina Mario, Frediani Bruno, Selmi Carlo, Rigante Donato, Cantarini Luca
Abstract excerpt
Ocular involvement is frequent in the monogenic autoinflammatory disorders and generally occurs as spontaneously recurring inflammatory events at different ocular sites caused by the aberrant release of proinflammatory cytokines, mainly IL-1β. Over the past decade, we witnessed a significant growth of eye abnormalities associated with idiopathic granulomatous disorders, familial Mediterranean fever, tumor...
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