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Article

CADASIL presenting with a behavioural variant frontotemporal dementia phenotype.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia - 1 Jan 2014

Alexander S K, Brown J M, Graham A, Nestor P J

Abstract excerpt

The behavioural variant of frontotemporal dementia (bvFTD) is characterised by personality change with a decline in cognition. We describe two patients with cerebral autosomal dominant arteriopathy with subcortical infarcts and leukencephalopathy (CADASIL) who presented with behavioural phenotypes similar to bvFTD. The first patient presented with progressive personality and behavioural change, had florid white...

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Identifiers

PMID: 24035425
DOI: 10.1016/j.jocn.2013.02.025

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026. Manifest publication-graph-cohort-2026-09-06.1.

Source receipt: pubmed, retrieved 6 Sept 2026.

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