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Article

Childhood-onset CADASIL: clinical, imaging, and neurocognitive features.

Journal of child neurology - 1 May 2010

Hartley Jessica, Westmacott Robyn, Decker Jochen, Shroff Manohar, Yoon Grace

Abstract excerpt

CADASIL (cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy) is a progressive neurodegenerative condition, associated with mutations in the notch3 gene. Symptoms include migraine with aura, mood disorders, progressive cognitive decline, subcortical ischemic strokes, dementia, and premature death. We present an 8-year-old boy with attention and behavioral difficulties, as...

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Source

Identifiers

PMID: 20197270
DOI: 10.1177/0883073810361382

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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