Article
Inclusion-body myositis and myopathies: different etiologies, possibly similar pathogenic mechanisms.
Current opinion in neurology - 1 Oct 2002
Askanas Valerie, Engel W King
Abstract excerpt
PURPOSE OF REVIEW: Sporadic inclusion-body myositis (s-IBM) and hereditary inclusion body myopathies are progressive muscle diseases that lead to severe disability. We discuss recent advances in illuminating their pathogenic mechanism(s). RECENT FINDINGS: We emphasize how different etiologies might lead to the strikingly similar pathology and possibly similar pathogenic cascade. Our basic hypothesis is that...
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