Article
Hemolytic uremic syndrome associated with Denys-Drash syndrome.
Pediatric nephrology (Berlin, Germany) - 1 Oct 2000
Sherbotie J R, van Heyningen V, Axton R, Williamson K, Finn L S, Kaplan B S
Abstract excerpt
The Denys-Drash syndrome is defined by the occurrence of combinations of pseudohermaphroditism, nephrotic syndrome with diffuse mesangial sclerosis, Wilms' tumor, and constitutional mutations in the WT1 suppressor gene. Most patients develop end-stage renal failure. Atypical hemolytic uremic syndrome (HUS) is defined by onset of acute hemolytic anemia with fragmented erythrocytes, thrombocytopenia, and renal...
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