Article
Peutz-Jeghers syndrome.
The American journal of gastroenterology - 1 Mar 2000
McGarrity T J, Kulin H E, Zaino R J
Abstract excerpt
Peutz-Jeghers syndrome (PJS) is an unusual polyposis syndrome that has enjoyed a rich and somewhat confusing history. Mucocutaneous pigmentation and diffuse gastrointestinal hamartomas are the hallmark features of this autosomal dominant inherited condition. Peutz-Jeghers syndrome is now also recognized as a cancer predisposition syndrome. In this review, we highlight the historical aspects of PJS polyposis with...
Topics
- Adenomatous Polyposis Coli
- Female
- Genetic Predisposition to Disease
- Humans
- Male
- Peutz-Jeghers Syndrome
- Precancerous Conditions
- Risk Factors