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Article

Characterization of the Pheochromocytoma-Predominant Subgroup of von Hippel-Lindau Disease.

Urology - 1 Jun 2025

Solomon Julie R, Lawson Keith A, Vocke Cathy D, Schmidt Laura S, Ricketts Christopher J, Linehan W Marston, Ball Mark W

Abstract excerpt

OBJECTIVE: To define a classification schema for von Hippel-Lindau (VHL) patients who have a pheochromocytoma predominant phenotyope. MATERIALS AND METHODS: VHL patients who underwent adrenalectomy with pathology-proven pheochromocytoma at our institution were included. We defined pheochromocytoma-predominant VHL a priori as patients with one or more of the following traits: early onset [age at first...

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Identifiers

PMID: 40090593
DOI: 10.1016/j.urology.2025.03.006
PMCID: PMC12146059

Genes

VHL

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026.

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