[Propranolol triggered recurrent ventricular tachycardia and electrical storm in an infant with long QT syndrome type 2].

Abstract excerpt

患儿　男，2月龄，因发现心率慢2个月，反复室性心动过速（VT）发作14 d伴发绀、精神反应差1 d就诊，临床出现多种心律失常，QT间期延长伴间歇性房室传导阻滞、交替性左束支与右束支传导阻滞及短VT，基因检测示KCNH2存在c.1478A>G杂合突变，诊断先天性长QT综合征2型，先后2次服用普萘洛尔未能有效控制VT且使其加重并形成电风暴，予静脉应用利多卡因后可有效终止电风暴，序贯美西律口服，同时予植入心脏起搏器，患儿未再发生恶性VT，随访11个月结局良好。.

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