Article
The determinants of survival among adults with cystic fibrosis-a cohort study.
Journal of physiological anthropology - 8 Nov 2021
Durda-Masny Magdalena, Goździk-Spychalska Joanna, John Aleksandra, Czaiński Wojciech, Stróżewska Weronika, Pawłowska Natalia, Wlizło Jolanta, Batura-Gabryel Halina, Szwed Anita
Abstract excerpt
BACKGROUND: Cystic fibrosis (CF) is one of the most common autosomal recessive diseases. Factors contributing to disease exacerbations and survival rate of CF patients are type of mutation in the CFTR gene, poor nutritional status, lung failure, and infection development by Pseudomonas aeruginosa. The study aimed to evaluate the relationship between the severity of mutation, nutritional status, lung function, and...
Topics
- Adolescent
- Adult
- Body Mass Index
- Cohort Studies
- Cystic Fibrosis
- Cystic Fibrosis Transmembrane Conductance Regulator
- Humans
- Lung
- Middle Aged
- Mutation
- Nutritional Status
- Prevalence
- Pseudomonas Infections