Article
Immunoglobulin A Vasculitis in a Japanese Patient with Complete Familial Mediterranean Fever Carrying MEFV Exon 10 Mutation.
The Tohoku journal of experimental medicine - 1 Oct 2021
Sasajima Tomomi, Fujita Yuya, Ejiri Yutaka, Suzuki Tomohiro, Wada Jun, Yokose Kohei, Yoshida Shuhei, Matsumoto Haruki, Asano Tomoyuki, Sato Shuzo, Yashiro-Furuya Makiko, Matsuoka Naoki, Temmoku Jumpei, Yago Toru, Watanabe Hiroshi, Migita Kiyoshi
Abstract excerpt
Immunoglobulin A (IgA) vasculitis is a systemic small-vessel vasculitis involving the skin, kidney, joints, and gastrointestinal tract. Familial Mediterranean fever (FMF) is the most common autoinflammatory disease characterized by periodic fever, peritonitis, pleuritis, or arthritis. It is well known that FMF may coexist with vasculitis, especially small and medium vessel vasculitis. Here we present a Japanese...
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