Congenital long QT syndrome: a clinician's guide.

Abstract excerpt

Congenital long QT syndrome (LQTS) is a familial cardiac ion channelopathy first described over 60 years ago. It is characterised by prolonged ventricular repolarisation (long QT on electrocardiography), ventricular arrhythmias and associated syncope or sudden cardiac death. As the most closely studied cardiac channelopathy, over the decades we have gained a deep appreciation of the complex genetic model of LQTS....

Topics

• Arrhythmias, Cardiac
• Death, Sudden, Cardiac
• Electrocardiography
• Humans
• Long QT Syndrome
• Phenotype