Article
Clinical Phenotypes of Sarcoidosis-Associated Pulmonary Hypertension.
Heart, lung & circulation - 1 Oct 2021
Mathijssen Harold, Huitema Marloes P, Bakker Annelies L M, Smits Fokko, Mager Johannes J, Snijder Repke J, Grutters Jan C, Post Marco C
Abstract excerpt
BACKGROUND AND OBJECTIVE: Pulmonary hypertension (PH) is a known complication of pulmonary sarcoidosis and its aetiology is unclear. Different pathophysiological mechanisms in sarcoidosis-associated pulmonary hypertension (SAPH) are known. Clinical phenotyping can aid clinicians in choosing the optimal treatment strategy. This study aimed to describe clinical phenotypes of SAPH and their characteristics. METHODS:...
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