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Article

Late-onset cerebral arteriopathy in a patient with incontinentia pigmenti.

Brain & development - 1 Apr 2021

Kanai Sotaro, Okanishi Tohru, Kawai Miki, Yoshino Go, Tsubouchi Yoshiko, Nishimura Yoko, Sakuma Hiroshi, Kurahashi Hiroki, Maegaki Yoshihiro

Abstract excerpt

BACKGROUND: Incontinentia pigmenti (IP) is an X-linked neurocutaneous disorder that can present with cerebral arteriopathy during early infancy. However, no previous reports have demonstrated arteriopathic manifestations during postinfantile childhood in patients with IP. PATIENT DESCRIPTION: We describe a case of IP in a 2-year-old girl who developed encephalopathic manifestations associated with influenza A...

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Identifiers

PMID: 33419638
DOI: 10.1016/j.braindev.2020.12.015

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026. Manifest publication-graph-cohort-2026-09-06.1.

Source receipt: pubmed, retrieved 6 Sept 2026.

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