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Article

Phenotypic severity scoring system and categorisation for prune belly syndrome: application to a pilot cohort of 50 living patients.

BJU international - 1 Jan 2019

Wong Daniel G, Arevalo Michelle K, Passoni Niccolo Maria, Iqbal Nida S, Jascur Thomas, Kern Adam J, Sanchez Emma J, Satyanarayan Arthi, Gattineni Jyothsna, Baker Linda A

Abstract excerpt

OBJECTIVE: To design a novel system of scoring prune belly syndrome (PBS) phenotypic severity at any presenting age and apply it to a large pilot cohort. PATIENTS AND METHODS: From 2000 to 2017, patients with PBS were recruited to our prospective PBS study and medical records were cross-sectionally analysed, generating individualised RUBACE scores. We designed the pragmatic RUBACE-scoring system based on six...

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PMID: 30113772
DOI: 10.1111/bju.14524
PMCID: PMC7368761

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