Article
Successful Total Pericardiectomy for Constrictive Pericarditis in the First Series of Japanese Patients With Mulibrey Nanism.
The Canadian journal of cardiology - 1 May 2018
Yasuhara Jun, Omori Sayu, Maeda Jun, Nakagawa Naomi, Kamada Masahiro, Kosaki Kenjiro, Aeba Ryo, Yamagishi Hiroyuki
Abstract excerpt
Patients with Mulibrey nanism (MUL) present with growth failure and multiple organ manifestations, and MUL is caused by mutations in TRIM37. In this article, we report on the first case series of Japanese patients with MUL who developed congestive heart failure due to constrictive pericarditis. Our case series suggests that early diagnosis and total pericardiectomy before adherence of the pericardium might...
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