Article
Management of patients with severe Epstein syndrome: Review of four patients who received living-donor renal transplantation.
Nephrology (Carlton, Vic.) - 1 Apr 2019
Hashimoto Junya, Hamasaki Yuko, Takahashi Yusuke, Kubota Mai, Yanagisawa Taketo, Itabashi Yoshihiro, Muramatsu Masaki, Kawamura Takeshi, Kumagai Naonori, Ohwada Yoko, Sakai Ken, Shishido Seiichiro
Abstract excerpt
AIM: Epstein syndrome is a hereditary disease characterized by macrothrombocytopaenia and progressive nephritis. The abnormality of the MYH9 gene has a strong relationship to the severity of the disease. Severe Epstein syndrome progresses to end-stage renal disease rapidly after adolescence. There is no established therapy. We sought to clarify appropriate management of Epstein syndrome nephropathy. METHODS:...
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