Article
[Familial Mediterranean fever--an important differential diagnosis in systemic juvenile chronic arthritis].
Zeitschrift fur Rheumatologie - 1 Jan 2000
Michels H, Häfner R, Vogel P
Abstract excerpt
Familial Mediterranean Fever (FMF), characterized by recurring episodes of fever, serositis, arthritis, skin changes and complicated by amyloidosis in 30%-60% of cases frequently begins in childhood. Systemic juvenile rheumatoid arthritis (systemic JRA, Still's disease) is the most important differential diagnosis. In our series of 10 patients the mean age of onset was 4.9 +/- 2.2 years (range 2-9 years). The...
Topics
- Adolescent
- Amyloidosis
- Arthritis, Juvenile
- Child
- Colchicine
- Diagnosis, Differential
- Familial Mediterranean Fever
- Female
- Humans
- Male
- Phenotype
