Article
Frequency of Cardiovascular Involvement in Familial Amyloidotic Polyneuropathy in Brazilian Patients.
Arquivos brasileiros de cardiologia - 1 Nov 2015
Queiroz Márcia Cavalcanti de Campos, Pedrosa Roberto Coury, Berensztejn Amanda Cardoso, Pereira Basílio de Bragança, Nascimento Emília Matos do, Duarte Martha Maria Turano, Pereira-Junior Pedro Paulo, Cruz Marcia Waddington
Abstract excerpt
BACKGROUND: Familial amyloidotic polyneuropathy (FAP) is a rare disease diagnosed in Brazil and worldwide. The frequency of cardiovascular involvement in Brazilian FAP patients is unknown. OBJECTIVE: Detect the frequency of cardiovascular involvement and correlate the cardiovascular findings with the modified polyneuropathy disability (PND) score. METHODS: In a national reference center, 51 patients were...
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